X.m
Pulmonary/systemic vasculopathy/vasculitis (ANCA status unknown or negative)
Older literature does not mention ANCA status (See under Xs). Can involve the lung, deep-seated organs (liver, kidney), viscerae, brain, extremities and/or skin or be diffuse (polyangiitis) clinically mimicking granulomatosis with polyangiitis (formerly known as Wegener's). See also under IIId and VId
Causative drugs
28
2
1